what-when-how
In Depth Tutorials and Information
TABLE 31.2
OI Registry Eye survey Results from the Kennedy
Krieger Institute
TABLE 31.2
OI Registry Eye survey Results from the Kennedy
Krieger Institute
TABLE 31.2
(Continued)
OI Type Breakdown
OI Type Breakdown
How
Many
How
Many
OI Type Breakdown
How
Many
Eye Condition
Eye Condition
%
%
OI Type
OI Type
How Many
How Many
Eye Condition
%
OI Type
How Many
lazy eye
2
0.5
III
1
glaucoma
10
2.4
I
5
IV
1
IV
2
high pressure
1
0.2
Unknown
1
Unknown
3
eyes do not close all the way
while sleeping
1
0.2
Unknown
1
keratoconus (thinning disorder
of cornea)
7
1.7
I
4
chorioretinitis
1
0.2
Unknown
1
Unknown
3
retinal “stretching”; thin border
between sclera and pupil
1
0.2
I
1
loss of vision
40
9.8
I
23
III
2
lasik correction
1
0.2
III
1
IV
3
macular degeneration
3
0.7
I
2
Unknown
12
IV
1
retinal or vitreous hemorrhages
(bleeding)
2
0.5
I
1
presbyopia
1
0.2
I
1
ptosis
1
0.2
IV
1
Unknown
1
paralysis in my right eye
1
0.2
I
1
retinal tears and (or)
detachment
1
0.2
IV
1
oculomotor nerve palsy
1
0.2
I
1
sensitive red eyes - allergies
1
0.2
I
1
scleromalacia (degenerative
scleral thinning)
3
0.7
I
2
ocular occlusion in my right eye
1
0.2
I
1
Unknown
1
Responses from OI Registry Eye Survey by Kennedy Krieger Institute from a total of
409 patients. Average age in years
+
/
−
SD
=
35.2
+
/
−
19.6. Sex % (N)
=
71% (290)
female; 29% (119) male. OI type % (N): I 50% (203); III 9% (35); IV 12% (50); V 2%
(6); VI 1% (2); Unknown 27% (111).
Other (please list):
dry eyes
1
0.2
I
1
near sighted
17
4.2
I
9
IV
2
This eye survey provides some insight into the prev-
alence of different eye conditions among the OI popu-
lation. However, as a survey, it does not document
disease severity, age of onset, treatments performed or
extent of visual loss. As all of the conditions listed can
be found outside of the OI population, these conditions
are not specifically associated with OI but some OI eyes
may be more at risk. The conditions listed are best diag-
nosed and treated by ophthalmologists with appropri-
ate subspecialty training.
Unknown
6
far sighted
4
1.0
I
2
Unknown
2
floaters
3
0.7
I
1
Unknown
2
cataract
9
2.2
I
6
Unknown
3
astigmatism
15
3.7
I
9
IV
1
GENERAL CONSIDERATIONS FOR OI
PATIENTS AND EYE CARE
V
1
Unknown
4
contacts needed
1
0.2
I
1
As outlined in this chapter, many structures in the
eye and visual system may be affected by OI. With cor-
neas being abnormally thin in many patients with OI,
refractive surgery should be approached with great
caution if at all. Abnormalities in collagen and corneo-
scleral architecture and strength may not respond nor-
mally to surgical intervention. Thin corneas may also
put some OI eyes at increased risk for glaucoma and
its progression. Refractive errors in OI eyes - myopia,
sensitivity to light
2
0.5
I
1
Unknown
1
eyes are slightly oval shaped,
not round
1
0.2
III
1
unknown rapid loss of vision at
the age of 40
1
0.2
I
1
(
Continued
)
